Myofibroblastoma survival rate

Myofibroblastoma is a relatively serious disease. If it is not given enough attention, it will affect the patient's life. Therefore, if the related disease has been diagnosed, we must alleviate it under the doctor's advice and guidance. This can alleviate the physical condition to a certain extent and promote life expectancy to a certain extent. Patients should actively seek treatment. So, what is the survival rate for myofibroblastoma?

1. It is common in children and adolescents, with an average age of 10 years old. It can also occur in adults, and is slightly more common in women. It occurs in soft tissues and internal organs and can be located anywhere in the body, with the most common sites being the lungs, greater omentum, and mesentery. The greater omentum is the most common site outside the lung, accounting for 43% of cases outside the lung. Other sites include soft tissue, mediastinum, gastrointestinal tract, pancreas, genitals, oral cavity, breast, nerves, bones and central nervous system.

2. Clinical manifestations

Depending on the site of onset, the onset is often insidious. Clinical symptoms are mostly caused by the tumor itself and its compression of surrounding organs. There may also be fever, weight loss, pain, anemia, thrombocytosis, accelerated erythrocyte sedimentation rate, etc. The clinical symptoms are similar to those of malignant tumors, but they lack specificity. Symptoms and signs often disappear after tumor resection.

3. Imaging Performance

The manifestations in different parts are diverse and lack specific signs.

1. IMT occurring in the lungs is a single lesion. Most of them are located under the peripheral pleura of the lungs.

2. The boundaries of central lesions are clearer. It may be accompanied by atelectasis, and calcifications of various shapes can be seen inside. Especially more common in children.

3. Peripheral lesions appear as irregular tumors. The tumor-lung interface is blurred. Thick and long spicules or thorn-like protrusions can be seen, which are different from the short spicules of lung cancer; at a certain level of the lesion, one side of the edge can be seen to be straight and knife-cut-like. That is, "straight expedition". It may be caused by traction of fibrosis at the edge of the lesion, or it may be related to the formation of the lesion along the edge of the lobe or segment; the edge of the lesion may also change into a sharp angle, which may be caused by pleural adhesion and fibrous tissue proliferation around the lesion; these signs can be used as a basis for distinguishing benign and malignant lung tumors.

Extrapulmonary IMT often presents as a single soft tissue tumor. Enhanced scans showed uniform or uneven moderate to significant enhancement, with no obvious specific manifestations.